Symptoms Of Friedreich's Ataxia

Muscle Weakness

Friedreich's ataxia attacks the neurons responsible for the actual voluntary movement of the muscles, and naturally, muscle weakness will occur as a result of the decreased mobility and decreased communication between the nerves in the limbs and the brain. The reduction in muscle strength will be symmetrical and progressive as the disease advances. Most often, the most severe weakening of the muscular system occurs in the muscles of the pelvic girdle region and then radiates down to the lower extremities. It is the combination of the weakening of the muscles and the progressive coordination loss that compels and causes most Friedreich's ataxia patients into using a wheelchair for mobility. Once an individual begins using a wheelchair because of the complications resulting from the disease, their muscle strength above the pelvis will usually stay unimpaired until the disease reaches more advanced stages. While the upper muscle strength is not a good indicator of how advanced the disease is, the strength and capabilities of the pelvic and leg muscles can help form a good idea of how far along Friedreich's ataxia has progressed.